INTRODUCTION

Amelogenesis imperfecta (AI) is a genetic disorder that affects the development and subsequent formation of enamel in the permanent dentition, primary dentition, or both. AI has been classified into 4 main types: hypoplastic (type 1), hypomaturation (type 2), hypocalcified (type 3), and hypomaturation, hypoplasia, and taurodontism (type 4) & also subclassified based on their gene mutation and their mode of inheritance. Clinical characteristics of enamel defects are variable, ranging in texture, color, and thickness. Conversely, teeth can also present as smooth, yellow- brown, and decreased in thickness. Both scenarios would indicate prosthodontic intervention despite the variation in presentation because rapid loss of tooth structure and subsequent loss of vertical dimension due to the defective enamel chipping off or flaking easily. Malocclusion and craniofacial features such as an anterior or posterior open occlusal relationship, constricted maxillary arch, or reversed curve of Spee may also be seen. Other clinical findings include high risk of caries, congenitally missing teeth, diastemas, compromised periodontal health, malformed teeth, and taurodontism. Such enamel defects not only affect the clinical appearance of the teeth but also have an overarching effect on the function, esthetics, and psychology of the affected patients particularly those in adolescence. Clinical management of patients with AI poses significant challenges regarding hard and soft-tissue management and psychosocial challenges, the timing of complete mouth rehabilitation in terms of patient’s age & compliance must also be considered. Consequently, conventionally luted complete coverage restorations have been recommended for the adolescent (and for the adult) patient. The use of completely digital workflows in complete mouth rehabilitation has been shown to reduce traditionally labor-intensive and lengthy treatment times, thereby potentially reducing the overall amount of time that patient with AI needs to spend in chair.

The purpose of this poster is to present full mouth fixed prosthodontic rehabilitation using digital dentistry protocols for a patient diagnosed with AI.
A 20-year-old young female patient with chief complaint of aesthetic correction of her teeth, diagnosed with Type 1 Hypoplastic AI presented for dental treatment. Full mouth fixed prosthodontic rehabilitation using fully digital dentistry protocol throughout the treatment process was planned for her to facilitate ease, precision and reduce conventionally and lengthy treatment with chair and lab time. Intraoral scans for preliminary diagnostics were used with CAD/CAM software to facilitate digital proposal of restorative plan.